{"id":5671,"date":"2022-05-27T14:06:05","date_gmt":"2022-05-27T12:06:05","guid":{"rendered":"https:\/\/webs.aspb.cat\/epidemiologia-transmissibles\/?page_id=5671"},"modified":"2026-08-19T10:51:43","modified_gmt":"2026-08-19T08:51:43","slug":"encefalopaties-espongiformes-transmissibles-humanes","status":"publish","type":"page","link":"https:\/\/webs.aspb.cat\/epidemiologia-transmissibles\/encefalopaties-espongiformes-transmissibles-humanes\/","title":{"rendered":"Encefalopaties espongiformes transmissibles humanes"},"content":{"rendered":"<div id=\"salmonellosi\" class=\"fusion-container-anchor\"><div class=\"fusion-fullwidth fullwidth-box fusion-builder-row-1 fusion-flex-container nonhundred-percent-fullwidth non-hundred-percent-height-scrolling\" style=\"--awb-border-radius-top-left:0px;--awb-border-radius-top-right:0px;--awb-border-radius-bottom-right:0px;--awb-border-radius-bottom-left:0px;--awb-padding-top:7%;--awb-padding-top-small:0px;--awb-flex-wrap:wrap;\" ><div class=\"fusion-builder-row fusion-row fusion-flex-align-items-center fusion-flex-content-wrap\" style=\"max-width:1295.4px;margin-left: calc(-2% \/ 2 );margin-right: calc(-2% \/ 2 );\"><div class=\"fusion-layout-column fusion_builder_column fusion-builder-column-0 fusion_builder_column_2_3 2_3 fusion-flex-column fusion-flex-align-self-flex-start\" style=\"--awb-bg-size:cover;--awb-width-large:66.666666666667%;--awb-margin-top-large:1.4em;--awb-spacing-right-large:1.47%;--awb-margin-bottom-large:0px;--awb-spacing-left-large:5.88%;--awb-width-medium:100%;--awb-order-medium:0;--awb-spacing-right-medium:0.98%;--awb-spacing-left-medium:0.98%;--awb-width-small:100%;--awb-order-small:2;--awb-spacing-right-small:0.98%;--awb-spacing-left-small:0.98%;\"><div class=\"fusion-column-wrapper fusion-column-has-shadow fusion-flex-justify-content-flex-start fusion-content-layout-column\"><div class=\"fusion-text fusion-text-1\"><p style=\"font-size: 16px; line-height: 1.76em; color: #181b20;\" data-fusion-font=\"true\">Les encefalopaties espongiformes transmissibles (EET) s\u00f3n un grup de malalties neurodegeneratives letals que afecten als animals i a les persones.<br \/>\nEs caracteritzen per un llarg per\u00edode d\u2019incubaci\u00f3 i una r\u00e0pida progressi\u00f3 fins a la mort.<\/p>\n<\/div><div class=\"fusion-text fusion-text-2 missio\"><div style=\"margin-top: 0px; margin-bottom: 26px; background-color: #fafafa;\">\n<p style=\"padding: 20px 40px 0px; color: #181b20; margin-bottom: .5em !important; font-size: 18px; font-weight: 300;\">La nostra missi\u00f3<\/p>\n<ul class=\"disseny-higienic-ul\" style=\"margin: 0px 40px; color: #181b20; padding-bottom: 20px !important;\">\n<li style=\"margin-bottom: 7px;\">Investigar totes les sospites d\u2019EET. En tots els casos, s\u2019ha de procurar confirmar el diagn\u00f2stic amb un estudi anatomopatol\u00f2gic.<\/li>\n<li style=\"margin-bottom: 7px;\">Controlar l\u2019evoluci\u00f3 epidemiol\u00f2gica de les EET.<\/li>\n<li style=\"margin-bottom: 7px;\">Controlar i fer seguiment dels brots d\u2019EET que es puguin produir a la comunitat.<\/li>\n<\/ul>\n<\/div>\n<\/div><div class=\"fusion-title title fusion-title-1 fusion-sep-none fusion-title-text fusion-title-size-three\" style=\"--awb-margin-top:26px;--awb-margin-bottom:26px;--awb-margin-top-small:16px;\" id=\"faqs\"><h3 class=\"fusion-title-heading title-heading-left fusion-responsive-typography-calculated\" style=\"margin:0;--fontSize:28;line-height:1.32;\"><strong>FAQS<\/strong><\/h3><\/div><div class=\"fusion-separator\" style=\"align-self: flex-start;margin-right:auto;width:100%;max-width:100&amp;amp;;\"><div class=\"fusion-separator-border sep-single sep-solid\" style=\"--awb-height:20px;--awb-amount:20px;border-color:rgba(40,45,51,0.1);border-top-width:1px;\"><\/div><\/div><div class=\"accordian fusion-accordian\" style=\"--awb-border-size:1px;--awb-icon-size:14px;--awb-content-font-size:14px;--awb-icon-alignment:right;--awb-hover-color:rgba(250,250,250,0.1);--awb-border-color:#ffffff;--awb-background-color:#ffffff;--awb-divider-color:rgba(40,45,51,0.1);--awb-divider-hover-color:rgba(40,45,51,0.1);--awb-icon-color:#181b20;--awb-title-color:#1d1d1b;--awb-content-color:#656a70;--awb-icon-box-color:#181b20;--awb-toggle-hover-accent-color:#181b20;--awb-title-font-family:&quot;Open Sans&quot;;--awb-title-font-weight:300;--awb-title-font-style:normal;--awb-title-font-size:18px;--awb-content-font-family:&quot;Open Sans&quot;;--awb-content-font-style:normal;--awb-content-font-weight:400;\"><div class=\"panel-group fusion-toggle-icon-right fusion-toggle-icon-unboxed\" id=\"accordion-5671-1\"><div class=\"fusion-panel panel-default panel-1be77f2c28464e6fc fusion-toggle-has-divider\"><div class=\"panel-heading\"><h4 class=\"panel-title toggle\" id=\"toggle_1be77f2c28464e6fc\"><a aria-expanded=\"false\" aria-controls=\"1be77f2c28464e6fc\" role=\"button\" data-toggle=\"collapse\" data-parent=\"#accordion-5671-1\" data-target=\"#1be77f2c28464e6fc\" href=\"#1be77f2c28464e6fc\"><span class=\"fusion-toggle-icon-wrapper\" aria-hidden=\"true\"><i class=\"fa-fusion-box active-icon awb-icon-minus\" aria-hidden=\"true\"><\/i><i class=\"fa-fusion-box inactive-icon awb-icon-plus\" aria-hidden=\"true\"><\/i><\/span><span class=\"fusion-toggle-heading\">Qu\u00e8 s\u00f3n les EET?<\/span><\/a><\/h4><\/div><div id=\"1be77f2c28464e6fc\" class=\"panel-collapse collapse \" aria-labelledby=\"toggle_1be77f2c28464e6fc\"><div class=\"panel-body toggle-content fusion-clearfix\">\n<p>Les encefalopaties espongiformes transmissibles (ETT) s\u00f3n un grup de malalties que causen lesions permanents al cervell i al sistema nervi\u00f3s fins a provocar la mort. Afecten als animals i a les persones.<br \/>\nEl nom prov\u00e9 de l\u2019aspecte d\u2019esponja que adquireix el teixit cerebral de les persones afectades.<\/p>\n<p>Aquestes malalties s\u00f3n causades per un pri\u00f3, una prote\u00efna an\u00f2mala coneguda com PrP<sup>c<\/sup>.<br \/>\nLes persones podem patir 5 malalties per prions:<\/p>\n<ul>\n<li><strong>La malaltia de Creutzfeldt-Jakob.<\/strong> \u00c9s la m\u00e9s freq\u00fcent i els s\u00edmptomes s\u00f3n semblants als de la dem\u00e8ncia.<\/li>\n<li><strong>La variant de la malaltia de Creutzfeldt-Jakob.<\/strong> Va apar\u00e8ixer a finals dels anys 90 i es va relacionar amb l\u2019encefalopatia espongiforme bovina (EBB), coneguda popularment com la \u201cmalaltia de les vaques boges\u201d.<\/li>\n<li><strong>La s\u00edndrome de Gerstmann-Str\u00e4ussler-Scheinker.<\/strong> \u00c9s una malaltia molt poc freq\u00fcent.<\/li>\n<li><strong>La kur\u00fa.<\/strong> Va ser a\u00efllada en persones d\u2019una tribu a Papua Nova Guinea i avui dia gaireb\u00e9 ha desaparegut. Es relacionava amb pr\u00e0ctiques rituals can\u00edbals.<\/li>\n<\/ul>\n<p>Aquestes malalties solen afectar persones grans, entre els 50 i 75 anys. A vegades, poden afectar persones m\u00e9s joves, sobretot dones.<br \/>\nEl per\u00edode d\u2019incubaci\u00f3 d\u2019aquestes malalties pot arribar a durar anys.<\/p>\n<p><strong>Els s\u00edmptomes de les EET s\u00f3n:<\/strong><\/p>\n<ul>\n<li>Canvis de personalitat<\/li>\n<li>Trastorns de salut mental, com depressi\u00f3 o ansietat<\/li>\n<li>Problemes de mem\u00f2ria i confusi\u00f3<\/li>\n<li>Insomni<\/li>\n<li>Tremolors i espasmes musculars<\/li>\n<li>\u00adDificultats per coordinar els moviments<\/li>\n<\/ul>\n<p>En la darrera etapa de la malaltia, la persona pateix defici\u00e8ncia mental greu i perd la capacitat de parlar i moure\u2019s.<\/p>\n<\/div><\/div><\/div><div class=\"fusion-panel panel-default panel-cdee4037d3ff81098 fusion-toggle-has-divider\"><div class=\"panel-heading\"><h4 class=\"panel-title toggle\" id=\"toggle_cdee4037d3ff81098\"><a aria-expanded=\"false\" aria-controls=\"cdee4037d3ff81098\" role=\"button\" data-toggle=\"collapse\" data-parent=\"#accordion-5671-1\" data-target=\"#cdee4037d3ff81098\" href=\"#cdee4037d3ff81098\"><span class=\"fusion-toggle-icon-wrapper\" aria-hidden=\"true\"><i class=\"fa-fusion-box active-icon awb-icon-minus\" aria-hidden=\"true\"><\/i><i class=\"fa-fusion-box inactive-icon awb-icon-plus\" aria-hidden=\"true\"><\/i><\/span><span class=\"fusion-toggle-heading\">Com es transmet?<\/span><\/a><\/h4><\/div><div id=\"cdee4037d3ff81098\" class=\"panel-collapse collapse \" aria-labelledby=\"toggle_cdee4037d3ff81098\"><div class=\"panel-body toggle-content fusion-clearfix\">\n<p>Nom\u00e9s l\u2019encefalopatia espongiforme bovina (EEB) o\u00a0 \u201cmalaltia de les vaques boges\u201d es pot transmetre a les persones a trav\u00e9s del consum de carn contaminada.<\/p>\n<p>Respecte a les altres malalties EET, no hi ha cap evid\u00e8ncia cient\u00edfica que es puguin transmetre a les persones.<\/p>\n<\/div><\/div><\/div><div class=\"fusion-panel panel-default panel-c9e396a2a56e821a8 fusion-toggle-has-divider\"><div class=\"panel-heading\"><h4 class=\"panel-title toggle\" id=\"toggle_c9e396a2a56e821a8\"><a aria-expanded=\"false\" aria-controls=\"c9e396a2a56e821a8\" role=\"button\" data-toggle=\"collapse\" data-parent=\"#accordion-5671-1\" data-target=\"#c9e396a2a56e821a8\" href=\"#c9e396a2a56e821a8\"><span class=\"fusion-toggle-icon-wrapper\" aria-hidden=\"true\"><i class=\"fa-fusion-box active-icon awb-icon-minus\" aria-hidden=\"true\"><\/i><i class=\"fa-fusion-box inactive-icon awb-icon-plus\" aria-hidden=\"true\"><\/i><\/span><span class=\"fusion-toggle-heading\">Quan s\u2019ha de consultar amb el metge\/essa?<\/span><\/a><\/h4><\/div><div id=\"c9e396a2a56e821a8\" class=\"panel-collapse collapse \" aria-labelledby=\"toggle_c9e396a2a56e821a8\"><div class=\"panel-body toggle-content fusion-clearfix\">\n<p>Si se sospita de la malaltia, cal consultar amb el metge o metgessa, que far\u00e0 el diagn\u00f2stic i en prescriur\u00e0 el tractament.<\/p>\n<\/div><\/div><\/div><div class=\"fusion-panel panel-default panel-9eba059982768b5ae fusion-toggle-has-divider\"><div class=\"panel-heading\"><h4 class=\"panel-title toggle\" id=\"toggle_9eba059982768b5ae\"><a aria-expanded=\"false\" aria-controls=\"9eba059982768b5ae\" role=\"button\" data-toggle=\"collapse\" data-parent=\"#accordion-5671-1\" data-target=\"#9eba059982768b5ae\" href=\"#9eba059982768b5ae\"><span class=\"fusion-toggle-icon-wrapper\" aria-hidden=\"true\"><i class=\"fa-fusion-box active-icon awb-icon-minus\" aria-hidden=\"true\"><\/i><i class=\"fa-fusion-box inactive-icon awb-icon-plus\" aria-hidden=\"true\"><\/i><\/span><span class=\"fusion-toggle-heading\">Com es pot prevenir?<\/span><\/a><\/h4><\/div><div id=\"9eba059982768b5ae\" class=\"panel-collapse collapse \" aria-labelledby=\"toggle_9eba059982768b5ae\"><div class=\"panel-body toggle-content fusion-clearfix\">\n<p>A les zones on hi ha EET, s\u2019han eliminat de la cadena aliment\u00e0ria els teixits bovins on hi poden haver prions: les am\u00edgdales, la gl\u00e0ndula timus, els ulls, l\u2019enc\u00e8fal, la medul\u00b7la espinal, la melsa, el mesenteri i l\u2019intest\u00ed prim.<\/p>\n<\/div><\/div><\/div><div class=\"fusion-panel panel-default panel-81f13204d7609b1da fusion-toggle-has-divider\"><div class=\"panel-heading\"><h4 class=\"panel-title toggle\" id=\"toggle_81f13204d7609b1da\"><a aria-expanded=\"false\" aria-controls=\"81f13204d7609b1da\" role=\"button\" data-toggle=\"collapse\" data-parent=\"#accordion-5671-1\" data-target=\"#81f13204d7609b1da\" href=\"#81f13204d7609b1da\"><span class=\"fusion-toggle-icon-wrapper\" aria-hidden=\"true\"><i class=\"fa-fusion-box active-icon awb-icon-minus\" aria-hidden=\"true\"><\/i><i class=\"fa-fusion-box inactive-icon awb-icon-plus\" aria-hidden=\"true\"><\/i><\/span><span class=\"fusion-toggle-heading\">Qu\u00e8 s\u2019ha de fer si apareix un cas d\u2019EET?<\/span><\/a><\/h4><\/div><div id=\"81f13204d7609b1da\" class=\"panel-collapse collapse \" aria-labelledby=\"toggle_81f13204d7609b1da\"><div class=\"panel-body toggle-content fusion-clearfix\">\n<p>Cal informar el Servei d\u2019Epidemiologia (SEPID), que ho comunicar\u00e0 a les autoritats sanit\u00e0ries auton\u00f2miques, estatals i europees.<\/p>\n<p>La Comissi\u00f3 Europea i els estats membres de la Uni\u00f3 Europea (UE) han adoptat diverses mesures per evitar casos d\u2019EET. Diverses lleis protegeixen les persones i els animals d&#8217;aquestes malalties. Totes les mesures de la UE sobre les EET animals es recullen en el <a href=\"https:\/\/eur-lex.europa.eu\/legal-content\/ES\/ALL\/?uri=CELEX:32001R0999\" target=\"_blank\" rel=\"noopener\">Reglament (CE) n\u00b0 999\/2001<\/a>.<\/p>\n<\/div><\/div><\/div><\/div><\/div><\/div><\/div><div class=\"fusion-layout-column fusion_builder_column fusion-builder-column-1 fusion_builder_column_1_3 1_3 fusion-flex-column fusion-flex-align-self-flex-start\" style=\"--awb-bg-size:cover;--awb-width-large:33.333333333333%;--awb-margin-top-large:1.4em;--awb-spacing-right-large:2.94%;--awb-margin-bottom-large:50px;--awb-spacing-left-large:11.76%;--awb-width-medium:100%;--awb-order-medium:0;--awb-margin-top-medium:0px;--awb-spacing-right-medium:0.98%;--awb-margin-bottom-medium:0px;--awb-spacing-left-medium:0.98%;--awb-width-small:100%;--awb-order-small:1;--awb-margin-top-small:0px;--awb-spacing-right-small:0.98%;--awb-margin-bottom-small:0px;--awb-spacing-left-small:0.98%;\" id=\"dades\"><div class=\"fusion-column-wrapper fusion-column-has-shadow fusion-flex-justify-content-flex-start fusion-content-layout-column\"><div class=\"fusion-title title fusion-title-2 fusion-sep-none fusion-title-text fusion-title-size-three\" style=\"--awb-margin-top:-5px;--awb-margin-bottom:-20px;--awb-sep-color:rgba(76,64,56,0.57);\"><h3 class=\"fusion-title-heading title-heading-left fusion-responsive-typography-calculated\" style=\"margin:0;--fontSize:28;line-height:1.32;\"><h1 style=\"text-align: left;\"><span style=\"color: #3b3737;\"><strong>Malalties relacionades<\/strong><\/span><\/h1><\/h3><\/div><div class=\"fusion-text fusion-text-3\"><ul>\n<li><a href=\"https:\/\/webs.aspb.cat\/epidemiologia-transmissibles\/toxiinfeccio-alimentaria\/\" target=\"_blank\" rel=\"noopener\"><strong><span style=\"color: #725ca0;\">Toxiinfeccions aliment\u00e0ries<\/span><\/strong><\/a><\/li>\n<\/ul>\n<\/div><div class=\"fusion-separator fusion-full-width-sep\" style=\"align-self: flex-start;margin-right:auto;margin-bottom:45px;width:100%;\"><\/div><div class=\"fusion-separator fusion-full-width-sep\" style=\"align-self: flex-start;margin-right:auto;margin-bottom:45px;width:100%;\"><\/div><div class=\"fusion-separator\" style=\"align-self: flex-start;margin-right:auto;width:100%;max-width:100&amp;amp;amp;amp;amp;amp;amp;;\"><div class=\"fusion-separator-border sep-single sep-solid\" style=\"--awb-height:20px;--awb-amount:20px;--awb-sep-color:rgba(157,157,156,0.3);border-color:rgba(157,157,156,0.3);border-top-width:1px;\"><\/div><\/div><div style=\"text-align:left;\"><a class=\"fusion-button button-flat fusion-button-default-size button-custom fusion-button-default button-1 fusion-button-default-span fusion-button-default-type botones-imp-com\" style=\"--button_accent_color:#181b20;--button_accent_hover_color:rgba(24,27,32,0.68);--button_border_hover_color:#780404;--button_gradient_top_color:#ffffff;--button_gradient_bottom_color:#ffffff;--button_gradient_top_color_hover:rgba(255,255,255,0.92);--button_gradient_bottom_color_hover:rgba(255,255,255,0.92);--button_text_transform:none;\" target=\"_self\" href=\"javascript:window.print()\"><span class=\"fusion-button-text awb-button__text awb-button__text--default\">Descarregar<\/span><i class=\"fa-print fas awb-button__icon awb-button__icon--default button-icon-right\" aria-hidden=\"true\"><\/i><\/a><\/div><div class=\"fusion-separator\" style=\"align-self: flex-start;margin-right:auto;width:100%;max-width:100&amp;amp;amp;amp;amp;amp;amp;;\"><div class=\"fusion-separator-border sep-single sep-solid\" style=\"--awb-height:20px;--awb-amount:20px;--awb-sep-color:rgba(157,157,156,0.3);border-color:rgba(157,157,156,0.3);border-top-width:1px;\"><\/div><\/div><\/div><\/div><\/div><\/div><\/div>\n","protected":false},"excerpt":{"rendered":"","protected":false},"author":1,"featured_media":0,"parent":0,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","meta":{"footnotes":""},"class_list":["post-5671","page","type-page","status-publish","hentry"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v26.8 - 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